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Washington University Experience | MYELIN (NON-IMMUNE MEDIATED) | Retinal Vasculopathy with Cerebral Leukoencephalopathy (RVCL, TREX1 Mutation) | 2C1 Cerebroretinal Vasculopathy (Case 2) 1_17

2C1,2 The kidneys are atrophic and scarred as seen in this external view and in cut section. There is severe global glomerulosclerosis and arteries and arterioles are markedly thickened with concentric layering and luminal narrowing.

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