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Washington University Experience | MYELIN (NON-IMMUNE MEDIATED) | Vanishing White Matter Dz | 2A0 Case 2
Case 2 History ---- This case is one of two Cree Leukoencephalopathy (CLE) affected families with neurologic onset resulting in mild motor developmental delay during early infancy followed by acute neurological deterioration during a febrile illness in infancy. Both patients died within 10 days of onset of acute neurological symptoms. The patient presented at age 4 months with developmental delay followed by progressive deterioration to a decerebrate, nonresponsive state by age 13 months and death 1 month later.
